Generalised lymphangiectasia: pulmonary presentation in an adult.
نویسندگان
چکیده
منابع مشابه
Congenital pulmonary lymphangiectasia
Congenital pulmonary lymphangiectasia (PL) is a rare developmental disorder involving the lung, and characterized by pulmonary subpleural, interlobar, perivascular and peribronchial lymphatic dilatation. The prevalence is unknown. PL presents at birth with severe respiratory distress, tachypnea and cyanosis, with a very high mortality rate at or within a few hours of birth. Most reported cases ...
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Primary pulmonary lymphangiectasia (PPL) is a rare disorder of unknown aetiology characterised by dilatation of the pulmonary lymphatics. PPL is widely reported to have a poor prognosis in the neonatal period and little is known about the clinical features of patients who survive the newborn period. The current authors report the outcome in nine patients diagnosed in infancy with PPL over a 15-...
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INTRODUCTION Nemaline myopathy is a rare genetic muscle disorder defined by the presence of nemaline rods in the muscle fibre sarcoplasm. Congenital nemaline myopathy is the most serious form of the disease's spectrum. CASE PRESENTATION The affected newborn has no spontaneous movement, fractures at birth and respiratory insufficiency. The present case was a Thai male, floppy at birth with fra...
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متن کاملCongenital Pulmonary Lymphangiectasia, Associated with Total Anomalous Pulmonary Venous Return
Congenital pulmonary lymphangiectasia (CPL) is a rare pathological diagnosis. It was first reported by Virchow in 1856. CPL is histologically characterized by pulmonary lymphatic dilatation without lymphatic proliferation in the subpleural, peribronchovascular and interlobular areas. The prognosis of CPL is very poor where approximately 50% of all infants are stillborn and most others usually d...
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ژورنال
عنوان ژورنال: Thorax
سال: 1996
ISSN: 0040-6376
DOI: 10.1136/thx.51.7.767